| 郭佳,任杰,李兴鹏,郝昆,孙莹,王仁贵,岳云龙.克利佩尔-特农纳(Klippel-Trenaunay)综合征伴发下肢淋巴水肿MR胸导管成像表现[J].中国医学影像技术,2026,42(5):737~741 |
| 克利佩尔-特农纳(Klippel-Trenaunay)综合征伴发下肢淋巴水肿MR胸导管成像表现 |
| MR thoracic ductography findings of Klippel-Trenaunay syndrome complicated with lower extremity lymphoedema |
| 投稿时间：2026-04-03 修订日期：2026-05-15 |
| DOI：10.13929/j.issn.1003-3289.2026.05.017 |
| 中文关键词: 克利佩尔-特农纳-韦伯综合征 淋巴水肿 磁共振成像 |
| 英文关键词:Klippel-Trenaunay-Weber syndrome lymphedema magnetic resonance imaging |
| 基金项目:北京世纪坛医院青年基金(2023-q24)。 |
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| 中文摘要: |
| 目的 观察克利佩尔-特农纳综合征合并下肢淋巴水肿(KTS-LEL)的MR胸导管成像(MRTD)表现。方法 回顾性分析47例KTS-LEL的MRTD资料,根据2020国际淋巴学会下肢淋巴水肿分期标准将其分为Ⅰ期(n=16)、Ⅱ期(n=12)及Ⅲ期(n=19)组;对比组间胸导管(包括胸导管主干、末端显影情况及胸导管末端形态)及淋巴干(包括支气管纵隔干、锁骨下干、腰干、髂干)显影状况。结果 47例中,33例(33/47,70.21%)胸导管主干显影正常、14例(14/47,29.79%)间断显影/不显影;35例(35/47,74.47%)胸导管末端显影、12例(12/47,25.53%)不显影。35例胸导管末端显影中,25例(25/35,71.43%)形态异常。Ⅱ、Ⅲ期组胸导管末端显影形态异常者占比、腰干和髂干异常显影者占比及腰干稀疏者占比均高于Ⅰ期组(P均＜0.05)。结论 MRTD中KTS-LEL可见中央淋巴管异常,且胸导管末端显影形态及淋巴干异常显影与下肢淋巴水肿分期有关。 |
| 英文摘要: |
| Objective To observe MR thoracic ductography (MRTD) findings of Klippel-Trenaunay syndrome complicated with lower extremity lymphoedema (KTS-LEL). Methods MRTD data of 47 patients with KTS-LEL were retrospectively analyzed. According to 2020 International Society of Lymphology staging criteria for lower extremity lymphedema, the patients were divided into stage Ⅰ (n=16), stage Ⅱ (n=12) and stage Ⅲ (n=19) groups. The visualization of thoracic duct including the main thoracic trunk, visualization of the terminal thoracic duct and morphology of the terminal thoracic duct, as well as the visualization of the major lymphatic trunks, including the bronchomediastinal, subclavian, lumbar and iliac trunks, were recorded and compared among groups. Results Among 47 cases, normal main thoracic duct was observed in 33 cases (33/47, 70.21%), while intermittent visualization or non-visualization of the main thoracic duct were noticed in 14 cases (14/47, 29.79%). The terminal thoracic duct was visualized in 35 cases (35/47, 74.47%) but not visualized in 12 cases (12/47, 25.53%). Among 35 cases with visualized terminal thoracic duct, abnormal terminal thoracic duct morphology was observed in 25 cases (25/35, 71.43%). The proportion of abnormal terminal thoracic duct morphology, abnormal visualization of the lumbar and iliac trunks, and of hypoplastic lumbar trunks were higher in stage Ⅱ and stage Ⅲ groups than in stage Ⅰ group (all P＜0.05). Conclusion MRTD findings of KTS-LEL mainly included central lymphatic abnormalities, and the morphology of visualized terminal thoracic duct and abnormal visualization of lymphatic trunks were associated with the stage of lower extremity lymphedema. |
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