| 李长健,李旭,胡克非,王晓玉,胡俊.儿童脂肪纤维瘤病CT及MRI表现[J].中国医学影像技术,2024,40(9):1395~1399 |
| 儿童脂肪纤维瘤病CT及MRI表现 |
| CT and MRI manifestations of lipofibromatosis in children |
| 投稿时间：2024-03-17 修订日期：2024-05-01 |
| DOI：10.13929/j.issn.1003-3289.2024.09.025 |
| 中文关键词: 儿童 纤维瘤病,侵袭型 体层摄影术,X线计算机 磁共振成像 |
| 英文关键词:child fibromatosis, aggressive tomography, X-ray computer magnetic resonance imaging |
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| 中文摘要: |
| 目的 观察儿童脂肪纤维瘤病(LPF)CT及MRI表现。方法 回顾性分析经病理证实LPF的16例患儿,观察其CT及MRI表现。结果 16例LPF中,4例病灶边界较清、12例边界不清,6例形态较规则、10例不规则,2例可见不完整包膜、14例无明显包膜。6例脂肪为主型LPF主要表现为中心散在部分纤维条索病灶或病灶一侧呈云絮状软组织密度/信号而无明显边界;8例纤维为主型病灶形态松散,周围伴多发纤细条索向周围延伸,内见部分散在囊状脂肪密度/信号;2例均衡型病灶主要表现边界较规则、清晰的混杂密度/信号。12例接受增强扫描,其中7例可见病灶内非脂肪区轻度渐进性强化,2例病灶周边明显强化、中心强化不明显,1例病灶明显均匀性强化,2例无明显强化;均未见明显钙化、囊变及骨质破坏。结论 CT及MRI中LPF多表现为皮下含脂密度/信号病变,常以脂肪细胞为主或纤维成分为主,呈轻度渐进性强化或明显强化,多无明显包膜、钙化、囊变及骨质破坏。 |
| 英文摘要: |
| Objective To observe CT and MRI manifestations of lipofibromatosis (LPF) in children. Methods Data of 16 children with LPF confirmed by pathology were retrospectively analyzed, and CT and MRI manifestations of lesions were observed. Results Among 16 cases, lesions with clear boundary were found in 4 cases but with unclear boundary in 12 cases, shaped regularly in 6 cases but irregularly in 10 cases, with incomplete capsule in 2 cases but without capsule in 14 cases. Fat predominant type lesions were detected in 6 cases, mainly characterized by scattered fibrous bands in the center or cloud like soft tissue density/signal on one side of lesion, without obvious boundary. Fibrous dominant type lesions were noticed in 8 cases, mainly present as loose morphology, multiple fibrous bands extending to surrounding area, with scattered cystic fat density/signal within the lesion. Balanced type LPF lesion was observed in 2 cases, mainly manifestated as regular shape mixed density/signal lesion with clear boundary. Among 12 cases who underwent enhanced scanning, mild progressive enhancement in the non-fat area were observed in 7 cases, obvious peripheral enhancement but not obvious central enhancement was found in 2 case, obvious homogeneous enhancement was noticed in 1 case, while no obvious enhancement was found in 2 cases. No obvious calcification, cystic changes nor bone destruction was detected. Conclusion CT and MRI manifestations of LPF included subcutaneous fat containing density/signal, often composed mainly of adipocytes or fibrous components, with mild progressive enhancement or significant enhancement, without obvious capsule, calcification, cystic changes nor bone destruction. |
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