王诗雅,韩建成,张烨,孙琳,王慧芳,何怡华.产前超声诊断胎儿永存左上腔静脉并右上腔静脉缺如畸形[J].中国医学影像技术,2018,34(5):715~718
产前超声诊断胎儿永存左上腔静脉并右上腔静脉缺如畸形
Prenatal ultrasonic diagnosis of fetal persistent left and absent right superior vena cava
投稿时间:2017-11-12  修订日期:2018-02-13
DOI:10.13929/j.1003-3289.201711072
中文关键词:  超声检查,产前  永存左上腔静脉  右上腔静脉缺如  胎儿
英文关键词:Ultrasonography, prenatal  Persistent left superior vena cava  Absent right superior vena cava  Fetus
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作者单位E-mail
王诗雅 深圳大学第一附属医院 深圳市第二人民医院超声科, 广东 深圳 518035
首都医科大学附属北京安贞医院超声心动图二部 胎儿心脏病母胎医学研究北京市重点实验室, 北京 100029 
 
韩建成 首都医科大学附属北京安贞医院超声心动图二部 胎儿心脏病母胎医学研究北京市重点实验室, 北京 100029  
张烨 首都医科大学附属北京安贞医院超声心动图二部 胎儿心脏病母胎医学研究北京市重点实验室, 北京 100029  
孙琳 首都医科大学附属北京安贞医院超声心动图二部 胎儿心脏病母胎医学研究北京市重点实验室, 北京 100029  
王慧芳 深圳大学第一附属医院 深圳市第二人民医院超声科, 广东 深圳 518035  
何怡华 首都医科大学附属北京安贞医院超声心动图二部 胎儿心脏病母胎医学研究北京市重点实验室, 北京 100029 heyihuaecho@hotmail.com 
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中文摘要:
      目的 探讨永存左上腔静脉并右上腔静脉缺如胎儿的产前超声特点及其诊断价值。方法 回顾性分析产前诊断为永存左上腔静脉并右上腔静脉缺如的8胎胎儿的超声资料,观察其超声表现及合并畸形,并随访其结局。结果 胎儿永存左上腔静脉并右上腔静脉缺如的超声特征为三血管-气管切面于肺动脉左侧见一血管回声,追踪走行见其汇入增宽的冠状静脉窦,同时主动脉右侧未见右上腔静脉显示。时间-空间关联成像(STIC)联合高分辨血流显像(HDF)可立体显示左上腔静脉与主动脉、肺动脉的空间位置关系。8胎均伴冠状静脉窦增宽,5胎合并其他心内畸形,1胎合并心外畸形。结论 超声可在产前准确诊断永存左上腔静脉并右上腔静脉缺如及合并畸形。冠状静脉窦扩张是产前超声诊断的重要线索。
英文摘要:
      Objective To investigate characteristics and value of prenatal ultrasound in diagnosing persistent left and absent right superior vena cava. Methods Ultrasonic data of 8 fetuses with persistent left and absent right superior vena cava were retrospectively analyzed. Ultrasonic findings of persistent left and absent right superior vena cava and other complicated anomalies were observed, and the outcomes were followed up. Results The ultrasonic characteristics of persistent left and absent right superior vena cava included a vessel which could be seen on the left of pulmonary artery on three vessel-trachea view draining into the dilated coronary sinus, and right superior vena cava was absent. With combined spatio-temporal image correlation (STIC) and high definition flow (HDF) technique, the spatial relationship of the left superior vena cava, aorta and pulmonary artery could be observed. Dilated coronary sinus was found in all 8 fetuses, other congenital heart defects were detected in 5 fetuses, and extracardiac anomaly was found in 1 fetus. Conclusion Persistent left and absent right superior vena cava and complicated anomalies can be accurately diagnosed with prenatal ultrasound. Dilated coronary sinus is an important clue for prenatal ultrasonic diagnosis.
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