朱向阳,陈欣林,杨小红,赵胜,杨文忠,冯倩,葛倩.胎儿心脏肿瘤与结节性硬化症的关系[J].中国医学影像技术,2014,30(7):1067~1070
胎儿心脏肿瘤与结节性硬化症的关系
Correlation between fetal cardiac tumors and tuberous sclerosis complex
投稿时间:2013-12-23  修订日期:2014-05-09
DOI:
中文关键词:  胎儿  超声检查,产前  磁共振成像  心脏肿瘤  结节性硬化症
英文关键词:Fetus  Ultrasonography, prenatal  Magnetic resonance imaging  Heare neoplasms  Tuberous sclerosis complex
基金项目:湖北省自然科学基金(2011CDA012)。
作者单位E-mail
朱向阳 湖北省妇幼保健院超声诊断科, 湖北 武汉 430070  
陈欣林 湖北省妇幼保健院超声诊断科, 湖北 武汉 430070 928339431@qq.com 
杨小红 湖北省妇幼保健院超声诊断科, 湖北 武汉 430070  
赵胜 湖北省妇幼保健院超声诊断科, 湖北 武汉 430070  
杨文忠 湖北省妇幼保健院 放射科, 湖北 武汉 430070  
冯倩 湖北省妇幼保健院超声诊断科, 湖北 武汉 430070  
葛倩 湖北省妇幼保健院超声诊断科, 湖北 武汉 430070  
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中文摘要:
      目的 探讨胎儿心脏肿瘤与结节性硬化症的关系。方法 回顾性分析产前超声发现胎儿心脏肿瘤的13胎超声及MRI资料。结果 13胎心脏肿瘤中,5胎为单发肿瘤,8胎为多发肿瘤;MRI发现颅内结节性硬化6胎,其中2胎心脏肿瘤为单发、4胎心脏肿瘤为多发。结论 胎儿心脏肿瘤多与结节性硬化症有关。产前超声发现胎儿心脏肿瘤时,应行产前颅脑MR检查,以早期诊断结节性硬化症。
英文摘要:
      Objective To explore the correlation between fetal cardiac tumors and tuberous sclerosis complex. Methods Totally 13 fetuses with cardiac tumors diagnosed with prenatal ultrasound underwent fetal MR examination, and the data were retrospectively analyzed . Results Among 13 fetuses, single cardiac tumor were detected in 5, and multiple tumors were found in 8 fetuses. Lesions of tuberous sclerosis complex were observed on brain MRI in 6 fetuses, including 2 with single cardiac tumor and 4 with multiple cardiac tumors. Conclusion Fetal cardiac tumors usually relate with tuberous sclerosis complex. Fetal brain MRI should be performed when cardiac tumors were noticed with prenatal ultrasound for early diagnosis of tuberous sclerosis complex.
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