| 郑楠楠,邵剑波,闫学强,方磊,周婧.影像学诊断Currarino综合征[J].中国医学影像技术,2014,30(5):661~664 |
| 影像学诊断Currarino综合征 |
| Imaging diagnosis of Currarino syndrome |
| 投稿时间：2013-11-28 修订日期：2014-03-05 |
| DOI： |
| 中文关键词: Currarino综合征 肛门直肠畸形 体层摄影术，X线计算机 磁共振成像 |
| 英文关键词:Currarino syndrome Anorectal malformation Tomography, X-ray computed Magnetic resonance imaging |
| 基金项目: |
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| 中文摘要: |
| 目的 探讨Currarino综合征的影像学表现。方法 回顾性分析经手术证实的9例Currarino综合征患儿的临床及影像学资料。对9例患儿均行腹部X线平片及消化道造影（或瘘管造影），8例行MSCT扫描，5例行骶尾部MR扫描。结果 9例中，6例为肛门闭锁，其中4例伴直肠会阴瘘；3例为肛门直肠狭窄。6例患儿一侧骶骨缺如，表现为“弯刀征”；2例表现为椎体融合；1例表现为骶尾骨短小，发育不良。5例骶前包块为畸胎瘤，4例为骶前脊髓脊膜膨出伴脊髓栓系。结论 Currarino综合征临床少见，但具有特征性影像学表现。对Currarino综合征患儿进行影像学检查并发现肛门直肠畸形时，应注意骶尾骨发育情况及有无骶前包块。 |
| 英文摘要: |
| Objective To investigate imaging performances of Currarino syndrome. Methods Clinical and imaging data of 9 Currarino syndrome patients confirmed by operation and pathology were retrospectively analyzed. All patients underwent KUB and gastrointestinal contrast (or fistula angiography), 8 underwent abdominal MSCT, 5 underwent sacrococcygeal MR scanning. Results In all patients, 6 had anal atresia, including 4 with scaphoid fossa fistula, 3 with anorectal stenosis. Six patients showed sacral agenesis on one side, displaying as "scimitar syndrome", 2 showed partial bone interbody fusion, 1 showed stunted sacrococcygeal bone. Presacral mass was proved teratoma in 5 patients, while in 4 patients were proved anterior sacral myelomeningocele with tethered cord. Conclusion Currarino syndrome is a rare disorder with characteristic imaging features. When anorectal malformation was detected, sacral bone development and presacral mass should be considered. |
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