| 刘文,蔡宗尧,于新华,陈宁.肝豆状核变性的颅脑MRI 诊断与鉴别诊断[J].中国医学影像技术,2000,16(12):1040~1042 |
| 肝豆状核变性的颅脑MRI 诊断与鉴别诊断 |
| Craniocerebral MRI Diagnosis and Differential Diagnosis on Hepatolenticular Degeneration |
| 投稿时间：2000-06-23 |
| DOI： |
| 中文关键词: 肝豆状核变性 磁共振成像 诊断 |
| 英文关键词:Hepatolenticular degeneration Magnetic Resonance Imaging Diagnosis |
| 基金项目: |
|
| 摘要点击次数: 1593 |
| 全文下载次数: 73 |
| 中文摘要: |
| 目的回顾性分析肝豆状核变性的MRI 诊断和主要鉴别诊断。方法本组30 例,男16 例,女14 例;临
床表现:行走不稳,言语不清,共济失调,肌张力改变。结果病变累及豆状核(30/ 30) 、尾状核(26/ 30) 、丘脑(17/
30) ,中脑(21/ 30) 、桥脑(17/ 30) 、丘脑外侧核(7/ 30) 和脑白质(4/ 30) ;脑萎缩以尾状核(14/ 30) 和桥脑(11/ 30) 为主。
结论基底节对称性异常信号伴有脑干病灶是肝豆状核变性的主要表现,鉴别诊断包括中毒性脑病和缺氧性脑病等。 |
| 英文摘要: |
| Objective MRI diagnosis and main differential diagnosis of hepatolenticular degeneration was analysed retrospectively. Methods 30 cases (16 male ,14 female) of hepatolenticular degeneration were diagnosed. Their clinical symptom includes walking unstable , speech disorder ,ataxia , dystonia. Results Nucleus lentiformis (30/ 30) ,caudate nucleus
(26/ 30) , thalamus (17/ 30) ,midbrain (21/ 30) ,pons (17/ 30) ,thalamus external nucleus (7/ 30) ,white matter of brain
(4/ 30) were the usual involve areas.Brain atrophy in caudate nucleus (14/ 30) and pons (11/ 30) can be seen as wall. Conclusion Main manifestation of hepatolenticular degeneration were abnormal signal in bilateral basal ganglia and brain stem.
Hepatolenticular degeneration should be differential diagnosed form toxic encephalopathy and anoxic encephalopathy. |
| 查看全文 查看/发表评论 下载PDF阅读器 |
|
|
|
