付茗,张群霞.超声诊断血友病肌肉病变进展[J].中国医学影像技术,2019,35(1):156~159 |
超声诊断血友病肌肉病变进展 |
Progresses of ultrasound in diagnosis of hemophilia muscular diseases |
投稿时间:2018-05-17 修订日期:2018-09-28 |
DOI:10.13929/j.1003-3289.201805103 |
中文关键词: 血友病 肌疾病 超声检查 |
英文关键词:hemophilia muscular diseases ultrasonography |
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中文摘要: |
血友病是一种性染色体连锁的隐性遗传性出血性疾病,主要临床表现为肌肉和关节反复出血。血友病肌肉病变可致急性筋膜间隔综合征、假性肿瘤形成、肌肉萎缩及骨化性肌炎等。超声检查具有实时、无创、简单快捷、可重复性强及分辨率高等优点,已广泛应用于诊断血友病肌肉病变。本文就超声在血友病肌肉病变诊断中的应用现状进行综述。 |
英文摘要: |
Hemophilia is a recessive hereditary hemorrhagic disease linked with sex chromosomes. The main clinical manifestations of hemophilia are repeated bleeding of muscles and joints. Hemophilia muscular diseases can cause acute compartment syndrome, pseudotumor formation, muscular atrophy and ossifying myositis. Ultrasonography has advantages of real-time, noninvasive, simple, quick, strong repeatability and high resolution, which has been widely used in diagnosis of hemophilia muscular diseases. The application progresses of ultrasound in diagnosis of hemophilia muscular diseases were reviewed in this article. |
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