黄楠,曹代荣,陈潭辉,林娜,吴吟晨,曾峥.头颈部淋巴结外Rosai-Dorfman病7例报告并文献复习[J].中国医学影像技术,2017,33(2):207~211
头颈部淋巴结外Rosai-Dorfman病7例报告并文献复习
Extra-nodal Rosai-Dorfman disease in head and neck: Seven cases report and literature review
投稿时间:2016-07-12  修订日期:2016-11-13
DOI:10.13929/j.1003-3289.201607056
中文关键词:  Rosai-Dorfman病  体层摄影术,X线计算机  磁共振成像
英文关键词:Rosai-dorfman disease  Tomography,X-ray computed  Magnetic resonance imaging
基金项目:
作者单位E-mail
黄楠 福建医科大学附属第一医院影像科, 福建 福州 350005  
曹代荣 福建医科大学附属第一医院影像科, 福建 福州 350005 dairongcao@163.com 
陈潭辉 福建医科大学附属第一医院影像科, 福建 福州 350005  
林娜 福建医科大学附属第一医院影像科, 福建 福州 350005  
吴吟晨 福建医科大学附属第一医院影像科, 福建 福州 350005  
曾峥 福建医科大学医学技术与工程学院, 福建 福州 350005  
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中文摘要:
      目的 分析头颈部淋巴结外Rosai-Dorfman病(RDD)的影像学表现。方法 回顾性分析7例经病理证实的头颈部淋巴结外RDD的影像学资料。结果 7例患者中,发生于眼眶3例,颅内2例,颅外1例,鼻腔1例。7例中除1例眼眶RDD伴颈部淋巴结肿大外,余6例均为单纯淋巴结外病变。3例眼眶病变表现为眼眶浸润性肿块,伴或不伴邻近骨质破坏;2例颅内病变发生于硬脑膜,T2WI呈明显低信号;1例颅外病变表现为帽状腱膜下软组织肿块,侵袭颅骨向颅内生长;1例鼻腔病变患者表现为鼻腔均质肿块。结论 头颈部淋巴结外RDD在不同部位可有不同的影像学表现,不具特征性。当发现颅内硬脑膜肿块、T2WI呈明显低信号、眼眶浸润性肿块以及鼻腔内占位时应考虑到RDD的可能。
英文摘要:
      Objective To analyze the image findings of extra-nodal Rosai-Dorfman disease (RDD) in the head and neck.Methods The image data of 7 RDD patients in the head and neck confirmed by pathology were analyzed retrospectively.Results The locations included orbit (n=3), intracranial area (n=2), extracranial region (n=1) and nasal cavity (n=1) in 7 RDD patients. Of the 7 RDDs, 6 manifested as pure extranodal disease without lymphadenopathy, except 1 patient in orbit. Three orbital RDDs demonstrated infiltrating mass with or without bone erosion; 2 intracranial RDDs demonstrated dura mater masses with extremely low signal intensity on T2WI; 1 extracranial RDD displayed subgaleal component with transcranial extension; 1 RDD of nasal cavity demonstrated homogenous soft tissue.Conclusion The image findings of extra-nodal RDD in the head and neck vary upon the location and lack typical characteristics. RDD should be taken into account in the presence of extra-axial dura mater mass with markedly low signal intensity on T2WI, infiltrating mass in the orbit and soft tissue in the nasal cavity.
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